@techreport{world_inequality_lab_world_2018,
title = {World inequality report 2018},
author = {World Inequality Lab},
url = {https://wir2018.wid.world/files/download/wir2018-summary-english.pdf},
year = {2018},
date = {2018-01-01},
pages = {296},
address = {Paris},
institution = {World Inequality Lab},
abstract = {Cardiomyopathies are a heterogeneous group of heart muscle disorders, being defined as "a myocardial disorder in which the heart muscle is structurally and/or functionally abnormal in the absence of coronary artery disease, hypertension, valvular disease and congenital heart disease sufficient to cause the observed mitochondriale myocardial abnormality". Four major types are recognised, namely the dilated, the hypertrophic and the restrictive variants, and arrhythmogenic right ventricular cardiomyopathy. A more recent approach divides the cardiomyopathies into a primary (only heart involvement) and a secondary group (systemic/ multi-organ involvement). Hypertrophic and dilated cardiomyopathy are the most frequent types in childhood. The diagnosis and work-up in patients with cardiomyopathy is complex and extensive. Familial and non-familial forms need to be differentiated. A broad family history (more than three generations) is necessary; a clinical screening of first-degree relatives is recommended. Gene mutations, inborn errors of metabolism, malformative syndromes and neuromuscular disease are well-known causes of cardiomyopathy. Still, a large part remains idiopathic. The diagnosis of cardiomyopathy in children requires a thorough anamnesis and clinical examination. A multidisciplinary approach is requested due to the large differential diagnosis. This is not only in the interest of the child, but even more given the possible involvement of other family members.},
keywords = {Desigualtats Socials, Informes, Mundial},
pubstate = {published},
tppubtype = {techreport}
}
Cardiomyopathies are a heterogeneous group of heart muscle disorders, being defined as "a myocardial disorder in which the heart muscle is structurally and/or functionally abnormal in the absence of coronary artery disease, hypertension, valvular disease and congenital heart disease sufficient to cause the observed mitochondriale myocardial abnormality". Four major types are recognised, namely the dilated, the hypertrophic and the restrictive variants, and arrhythmogenic right ventricular cardiomyopathy. A more recent approach divides the cardiomyopathies into a primary (only heart involvement) and a secondary group (systemic/ multi-organ involvement). Hypertrophic and dilated cardiomyopathy are the most frequent types in childhood. The diagnosis and work-up in patients with cardiomyopathy is complex and extensive. Familial and non-familial forms need to be differentiated. A broad family history (more than three generations) is necessary; a clinical screening of first-degree relatives is recommended. Gene mutations, inborn errors of metabolism, malformative syndromes and neuromuscular disease are well-known causes of cardiomyopathy. Still, a large part remains idiopathic. The diagnosis of cardiomyopathy in children requires a thorough anamnesis and clinical examination. A multidisciplinary approach is requested due to the large differential diagnosis. This is not only in the interest of the child, but even more given the possible involvement of other family members.
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